A case report on type I sturge weber syndrome with bilateral port-wine stain

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Case Report

Author Details : Vikas Agrawal, Nissi Chrysolite Gongati*, Srinivasulu Poluru

Volume : 8, Issue : 4, Year : 2022

Article Page : 279-281

https://doi.org/10.18231/j.ijn.2022.054

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Abstract

Sturge-Weber syndrome (SWS) is a type of neuro-cutaneous diseases which is seen in 1 in 50,000 populations and affects both the sexes equally. It usually manifests with a facial Port Wine Stain (PWS). Facial port-wine stains are usually isolated findings, however, when associated with cerebral and ocular vascular malformations they form part of the classical triad of Sturge-weber syndrome (SWS). The prevalence of PWS is estimated at three to five children per 1000 live births; there are ~26 million people worldwide with PWS birthmarks. The majority of facial PWS (~90%) are unilateral in a trigeminal dermatomal distribution. Here, we report a case of 39 years old female with SWS who presented with classical triad of SWS i.e., bilateral port-wine stain, epilepsy and severe glaucoma.
 

Keywords: Bilateral port­wine stain, epilepsy, glaucoma

How to cite : Agrawal V, Gongati N C, Poluru S, A case report on type I sturge weber syndrome with bilateral port-wine stain. IP Indian J Neurosci 2022;8(4):279-281

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